The rare Denys-Drash syndrome infant succeeds in being rescued the institute in Shanghai

The rare Denys-Drash syndrome infant succeeds in being rescued the institute in Shanghai
Www.chinanews.com's Shanghai, November 19 (Reporter Chen Jing) A boy who suffers from rare Denys-Drash syndrome succeeds in accepting the renal transplantation treatment in Shanghai recently. Today, he will recover and leave hospital, will begin the new life.
It is introduced, Denys-Drash syndrome is a kind of very rare inborn disease, the whole world reports about 200 so far, China nearly has 20 examples. 1967, Denys and the intersection of Drash and doctor,etc. suffer from nephropathy, the intersection of two sexes and deformity and the intersection of kidney and the intersection of master cell and the intersection of tumour and case of children, describe this kind of disease with one for the first time. This kind of disease regards nephropathy and syndrome as to mainly behave, with one of the male pseudohermaphrodism, kidney master cell tumour or the two. The pathology of nephropathy is that it turns a main characteristic, take place within two years old more that the membrane is hard in order to the filling the air, the kidney declines the death to develop until latter stage of end quickly.
The ones that were born in October of two or four years were checked the genital deformity of going outside once borning, leave splitting for the urethra. In a year old, have accepted that draw fixation under the left testis of peritoneoscope, has shifted down the left testis from abdominal cavity to the groin. The little child who has just resumed has presented edema of eyelid again, symptom of the urine with much bubble. Puncture and examine alive according to dual side kidneys, is diagnosed as as " cooking stove ball and segment sclerosis glomerulus disease of the office " ,Keep treating by taking medicine, but the result has been less than satisfactory all the time. To take medicine, treat time, make unable life like normal child over three o'clock.
In March of this year, the condition worsens, his repeated belly pains, urinates and reduces gradually. Five parents go to a doctor hospital he again every month. The little child is diagnosed as and suffered from extremely rare Denys-Drash syndrome, and lead to the fact the chronic renal function is not complete this time.
The pediatrics expert Xu Hong begins to consider in order to carry on relative's renal transplantation. Chinese renal transplantation expert's Vice President, bright red and jade professor of urology surgery of the hospital Zhongshan tell reporters, renal transplantation is the only possible means of livelihood. After being successful with mother's mixing type, on October 26, were pushed into the operating room with mother, the doctors will carry on relative the same kind of allogenic normal position renal transplantation skills who will create history for the two of mother and son.
It is introduced, the experts break through the technological difficulty smoothly, plant mother's kidney into the body carefully, five hours later, the operation is finished smoothly. The postoperative fourth day, it is small because of child's age, the ill physique is bad for a long time, the condition has presented repeatedly, the expert of hospital of Zhongshan has succeeded in removing all clots in the body of its through the operation again, have obtained success of this highly difficult operation completely.
Today, will recover and leave hospital. The doctor says, he can live as normal child in the future.
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